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영남의대학술지 Vol.28 No.1 p70-76, June2011
Case Report
전이성 고환주위 폐포성 횡문근육종 1예
Paratesticular Alveolar Rhabdomyosarcoma with Multiple Lymph Nodes Metastasis Successfully Treated with Chemotherapy
이하영, 현명수, 이경희, 김민경, 고성애, 손세훈, 박성우, 김동근, 김명진, 장효진, 김미진1
영남대학교 의과대학 내과학교실, 병리학교실1
교신저자：현명수, 대구광역시 남구 대명5동 317-1, 영남대학교 의과대학 내과학교실
Tel: (053) 620-3830, Fax: (053) 654-8386
E-mail : hms@med.yu.ac.kr
June 30, 2011
Abstract
Rhabdomyosarcomas are soft tissue sarcomas; while extremely rare in adults, they are one of the most common neoplasms in children and adolescents. Histologically, they can be classified into embryonal(ERMS), alveolar(ARMS), pleomorphic, and undifferentiated types. The ARMS type is very rare, and is associated with a poor prognosis. Common primary sites of ARMS are the trunk and extremities. We report on a case of paraaortic, supraclavicular, and axillary lymph node metastasis from paratesticular ARMS treated with VAC(vincristine, dactinomycin, cyclophosphamide)/ IE(ifosfamide, etoposide) chemotherapy in a young adult. Administration of six cycles of chemotherapy with VAC/ IE resulted in complete remission. The patient has maintained complete remission over the past 27 months.
Key Words: Rhabdomyosarcoma, Alveolar, Lymphatic Metastasis
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